Síndrome de Doege – Potter: Un reporte de caso  :  Doege-Potter Syndrome: A case report

Patricia Segura Nuñez; Fernando Monge Espinoza; Mayra  Orihuela Baldeon

doi:10.25176/RFMH.v24i4.6515

Authors

Patricia Segura Nuñez Department of Pulmonology, Hipólito Unanue National Hospital. Lima, Peru
Fernando Monge Espinoza Department of Pulmonology, Hipólito Unanue National Hospital. Lima, Peru
Mayra Orihuela Baldeon Department of Pulmonology, Hipólito Unanue National Hospital. Lima, Peru

DOI:

https://doi.org/10.25176/RFMH.v24i4.6515

Keywords:

Doege-Potter Syndrome, Solitary Fibrous Tumor, Hypoglycemia

Abstract

Doege-Potter syndrome is a rare paraneoplastic syndrome characterized by a benign or malignant mesenchymal tumor associated with persistent hypoglycemia. We present the case of a 70-year-old woman with a 4-year illness characterized by productive cough, oppressive pain in the left hemithorax, and progressively increasing dyspnea. The chest tomography revealed an extensive solid tumor in the lower 2/3 of the left hemithorax. An ultrasound-guided transthoracic biopsy of the tumor was performed. The histopathological study reports a solitary fibrous tumor and immunohistochemistry: STAT6 positive. Therefore, she underwent a thoracotomy with excision of the tumor. After surgery, glucose values normalized. The patient met the criteria for Doege-Potter syndrome, a rare entity.

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Author Biographies

Patricia Segura Nuñez, Department of Pulmonology, Hipólito Unanue National Hospital. Lima, Peru

Pulmonologist doctor

Fernando Monge Espinoza, Department of Pulmonology, Hipólito Unanue National Hospital. Lima, Peru

Pulmonologist doctor

Mayra Orihuela Baldeon, Department of Pulmonology, Hipólito Unanue National Hospital. Lima, Peru

Pulmonologist doctor

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